Kongenitte portosystemiske shunter, diagnose og behandling af en multisystemisk sygdom hos børn

Translated title of the contribution: Diagnosis and treatment of a multisystemic disorder in children called congenital portosystemic shunts

Abstract

Congenital portosystemic shunts (CPSS) are rare malformations, which connect the portal venous system and the systemic circulation. The disorder is discovered at prenatal screening, neonatal cholestasis as an incidental finding or by systemic complications such as pulmonary hypertension, encephalopathies or liver nodules. CPSS are associated to cardiac malformations and several syndromes. Intervention radiology plays a key role in treatment by closure of the shunt, which is indicated, if the patient has complications, the shunt is extrahepatic, or it is still persistent at two years of age, using a two-step approach, as summarised and discussed in this review.

Translated title of the contributionDiagnosis and treatment of a multisystemic disorder in children called congenital portosystemic shunts
Original languageDanish
Article numberV01210041
JournalUgeskrift for Laeger
Volume183
Issue number31
ISSN0041-5782
Publication statusPublished - 2 Aug 2021

Fingerprint

Dive into the research topics of 'Diagnosis and treatment of a multisystemic disorder in children called congenital portosystemic shunts'. Together they form a unique fingerprint.

Cite this