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Change in muscle strength over time in spinal muscular atrophy types II and III. A long-term follow-up study

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Whether muscle strength deteriorates with time in spinal muscular atrophy (SMA) types II and III is still debated. We present a long-term follow-up study on muscle strength in 30 patients with SMA types II and III. Median follow-up time was 17 years. Median number of assessments was four. All patients were assessed by Manual Muscle Testing (MMT), Brooke upper limb scale and EK scale. There was a difference in muscle strength of the upper limbs from first to last assessment in SMA II (p
Original languageEnglish
JournalNeuromuscular Disorders
Volume22
Issue number12
Pages (from-to)1069-74
Number of pages6
ISSN0960-8966
DOIs
StatePublished - 2012

ID: 36858162