TY - JOUR
T1 - Hybridbehandling af proteintabende enteropati hos patient med univentrikulærtkredsløb
AU - Holm-Weber, Thomas
AU - Gjedsted, Jacob
AU - Schmidt, Michael Rahbek
AU - Helvind, Morten
AU - Hjortdal, Vibeke E
PY - 2022/8/15
Y1 - 2022/8/15
N2 - Protein-losing enteropathy (PLE) is a severe Fontan complication. This is a case report of the first hybrid treatment of PLE in Denmark of an 11-year-old Fontan patient with severe symptoms (diarrhoea, fatigue and swelling) and low albumin level. Diagnostics included intranodal and intrahepatic dynamic contrast magnetic resonance lymphangiography. The hybrid intervention consisted of selective lymphatic duct embolisation and innominate vein turn-down to treat PLE. The interventions went well, and two months after discharge the patient was relieved from PLE symptoms, the albumin level was normalised, and the patient felt more energetic.
AB - Protein-losing enteropathy (PLE) is a severe Fontan complication. This is a case report of the first hybrid treatment of PLE in Denmark of an 11-year-old Fontan patient with severe symptoms (diarrhoea, fatigue and swelling) and low albumin level. Diagnostics included intranodal and intrahepatic dynamic contrast magnetic resonance lymphangiography. The hybrid intervention consisted of selective lymphatic duct embolisation and innominate vein turn-down to treat PLE. The interventions went well, and two months after discharge the patient was relieved from PLE symptoms, the albumin level was normalised, and the patient felt more energetic.
KW - Albumins
KW - Child
KW - Fontan Procedure/adverse effects
KW - Heart Defects, Congenital/complications
KW - Humans
KW - Postoperative Complications/etiology
KW - Protein-Losing Enteropathies/diagnosis
UR - https://ugeskriftet.dk/videnskab/hybridbehandlingafproteintabendeenteropati-hos-patient-med-univentrikulaertkredslob
M3 - Tidsskriftartikel
C2 - 36065879
VL - 184
JO - Ugeskrift for Laeger
JF - Ugeskrift for Laeger
SN - 0041-5782
IS - 33
M1 - V04220241
ER -