Tredjegradsatrioventrikulært blok hos en ung kvinde med kongenit centralt hypoventilationssyndrom

Rikke Hagelberg, Ulrik Dixen

Abstract

Congenital central hypoventilation syndrome (CCHS) is a rare multisystem disorder characterized by autonomic nervous system dysfunction, which often manifests as failure to maintain ventilatory homeostasis during sleep. We present a case with a third degree atrioventricular block in a young woman with CCHS, which to our knowledge has not been seen before. As sudden death is known to occur among patients with CCHS, and it is under consideration to offer regularly monitoring of patients throughout childhood and adolescence.

Bidragets oversatte titelThird degree atrioventricular block in a young woman with congenital central hypoventilation syndrome
OriginalsprogDansk
TidsskriftUgeskrift for Laeger
Vol/bind177
Udgave nummer2A
Sider (fra-til)16-7
Antal sider2
ISSN0041-5782
StatusUdgivet - 26 jan. 2015

Emneord

  • Atrioventricular Block
  • Electrocardiography
  • Female
  • Humans
  • Hypoventilation
  • Pacemaker, Artificial
  • Sleep Apnea, Central
  • Young Adult

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