Susacs syndrom er en vigtig differentialdiagnose ved monosymptomatisk encefalopati hos yngre voksne.

Caroline Ellinore Weinsjö, Gitte Buhl-Jensen, Marianne Wegener, Christoffer Tanderup Nielsen, Daniel Kondziella

Abstract

This is a case report of a 29-year-old man, who presented with progressive confusion, memory problems and personality changes during 1.5 months. Later, he developed bilateral hearing impairment but had no visual symptoms. A brain MRI showed numerous small hyperintensities in both hemispheres, a retinal fluorescence angiography revealed multiple hyperfluorescent arterial occlusions, and an audiogram showed bilateral hearing impairment. The patient was treated for Susac syndrome with high-dose corticosteroids initially, followed by intravenous immunoglobulin and cyclophosphamide.

Bidragets oversatte titelSusac syndrome is an important differential diagnosis in monosymptomatic encephalopathy in young adults
OriginalsprogDansk
TidsskriftUgeskrift for Laeger
Vol/bind181
Udgave nummer15
Sider (fra-til)V08180541
ISSN0041-5782
StatusUdgivet - 8 apr. 2019

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