@article{d8d166155b18486597c969ee11f6b4b8,
title = "Outcome of elexacaftor/tezacaftor/ivacaftor therapy in patients with cystic fibrosis and solid organ transplantation",
abstract = "We report a case series of four patients with cystic fibrosis (CF) and previous solid organ transplantation (SOT) receiving elexacaftor/tezacaftor/ivacaftor therapy for 6 months or more. Data was collected retrospectively. The treatment was well tolerated and all patients reported subjective improvements.",
keywords = "CFTR therapy, cystic fibrosis, cystic fibrosis transmembrane conductance regulator therapy, ETI, solid organ transplantation, Double-Blind Method, Humans, Organ Transplantation, Aminophenols, Cystic Fibrosis Transmembrane Conductance Regulator/genetics, Benzodioxoles/adverse effects, Cystic Fibrosis/drug therapy, Chloride Channel Agonists, Retrospective Studies, Mutation, Drug Combinations",
author = "{\O}rum, {Matilde B} and R{\"o}nsholt, {Frederikke F} and Majbritt Jeppesen and Elisabeth Bendstrup and Katzenstein, {Terese L} and Peter Ott and Michael Perch and Tacjana Pressler and Tavs Qvist and S{\o}ren Jensen-Fangel",
note = "This article is protected by copyright. All rights reserved.",
year = "2023",
month = feb,
doi = "10.1002/ppul.26217",
language = "English",
volume = "58",
pages = "602--605",
journal = "Pediatric Pulmonology",
issn = "8755-6863",
publisher = "John/Wiley & Sons, Inc. John/Wiley & Sons Ltd",
number = "2",
}