Low disease prevalence and inappropriate implantable cardioverter defibrillator shock rate in Brugada syndrome: a nationwide study

Anders Gaarsdal Holst, Henrik Kjærulf Jensen, Ole Eschen, Finn Lund Henriksen, Jørgen Kanters, Henning Bundgaard, Jesper Hastrup Svendsen, Stig Haunsø, Jacob Tfelt-Hansen

    32 Citationer (Scopus)

    Abstract

    Brugada syndrome (BrS) is an inherited channelopathy that predisposes to malignant ventricular arrhythmias and thereby syncope and sudden cardiac death. Prior studies characterizing BrS patients have used highly selected referral populations from tertiary centres and prevalence estimates have been carried out using electrocardiogram (ECG) surveys only. We aimed to identify and characterize all diagnosed BrS patients in Denmark (population 5.4 million).
    OriginalsprogEngelsk
    TidsskriftEuropace
    Vol/bind14
    Udgave nummer7
    Sider (fra-til)1025-9
    Antal sider5
    ISSN1099-5129
    DOI
    StatusUdgivet - 2012

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