Abstract
The European pediatric Soft tissue sarcoma Study Group analyzed all children with epithelioid hemangioendothelioma prospectively registered in the NRSTS-05 (EUDRACT 2005-001139-31) and in MTS-2008 (NCT00379457) studies: 10 patients with localized and one with metastatic disease. Median age was 14.3 years (range, 9.0-18.8). Local therapy was initial primary surgery in seven cases, and five patients received systemic therapy. No patients received radiotherapy. After a median follow-up of 50 months (range, 6-176) for living patients, nine patients remain alive off therapy and two died. Five-year progression free and overall survivals are, respectively, 77.1% (95% confidence interval [CI]: 34.5-93.9) and 74.1% (95% CI: 28.1-93.0).
Originalsprog | Engelsk |
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Artikelnummer | e29882 |
Tidsskrift | Pediatric Blood & Cancer |
Vol/bind | 69 |
Udgave nummer | 10 |
Sider (fra-til) | 1-4 |
Antal sider | 4 |
ISSN | 1545-5009 |
DOI | |
Status | Udgivet - okt. 2022 |